Case Report Recalcitrant scalp and intertriginous rash in a patient with diabetes insipidus: diversity of cutaneous manifestations and pitfalls in diagnosis of adult Langerhans histiocytosis
نویسنده
چکیده
Block 6 Level 9, Dermatology Unit, Singapore General Hospital, Outram Road, 169608, Singapore Langerhans cell histiocytosis (LCH) is a proliferative histiocytic disorder of unknown cause characterized by the accumulation of Langerhan cells in various tissues. Typically a disorder of childhood, features of this disease have been well documented in children but remain ambiguous and poorly documented in adults leading to many pitfalls in diagnosis. We report a case of Langerhans cell histiocytosis in a young lady who presented with cutaneous involvement of varying morphology and review the various cutaneous manifestations of adult Langerhans cell histiocytosis reported in the literature to date.
منابع مشابه
Langerhans cell Histiocytosis: Report of a case with cutaneous lesions with favorable response to oral Thalidomide
We report of a 29-year-old man presented with yellow-red, scaling papules on the skin of scalp, retro-auricular folds, inguinal, axillary, chest and abdomen. The lesions had a poikilodermatious appearance in some areas, such as trunk. The patient also had diabetes insipidus and skull osteolytic lesions. The diagnosis of langerhans cell histiocytosis (LCH) was suggested based on H and E staining...
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